CASES OF CHOREA
نویسندگان
چکیده
منابع مشابه
Sydenham chorea: MR manifestations in two cases.
The acute onset of a unilateral choreiform movement disorder in a child with a recently documented febrile illness or streptococcal pharyngitis is suggestive of Sydenham chorea. The MR manifestations of two clinically corroborated cases of Sydenham chorea are summarized . Increased signal intensity in the corpus striatum contralateral to the patients ' symptomatic side was observed on T2-weight...
متن کاملChorea-acanthocytosis: report of three cases from Iran.
Chorea-acanthocythosis (ChAc) is an inherited neurodegenerative disorder characterized by movement disorders, neuropsychiatric disturbances, neuropathy, myopathy, seizures and acanthocytosis accompanied by an elevated serum creatine kinase (CK) level. Its causative gene (VPS13A) produces chorein which is absent in ChAc patients as evaluated by Western blot assay. We report the first three Irani...
متن کاملSydenham's Chorea
Sydenham’s chorea is a delayed complication of group Aßhaemolytic streptococcal infections and forms one of the majorcriteria of acute rheumatic fever.It is characterised bychorea, muscular weakness, and a number of neuropsychiatricsymptoms. It is considered to be an autoantibody mediated disorderwith the evidence suggesting that patients with Sydenham’schorea produce antibodies that cross reac...
متن کاملHuntington's chorea.
The pharmacological treatment of Huntington's chorea has been based on the use of neuroleptic drugs, on the hypothesis that there is a functional dopaminergic hyperactivity in this illness (Agid, 1975). More recently, after the observation of reduced cholinergic and GABAminergic activity at the striatal level in brains of choreic subjects (McGeer et al., 1973; Stahl and Swanson, 1974; Bird and ...
متن کاملHuntington's chorea. Report of 3 cases and review of the literature.
Three cases of Huntington's chorea with onset before age 10 years are reported. Each child presented with rigidity and indistinct speech, and there was progressive deterioration. Necropsy examination confirmed the diagnosis in 2 of them. A review of reports showed a further 43 cases with onset before 10 years. The rigid variety of disease was seen most often, but isolated chorea and isolated pr...
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ژورنال
عنوان ژورنال: Brain
سال: 1884
ISSN: 0006-8950,1460-2156
DOI: 10.1093/brain/7.2.250